| 51 |
23846788 | Influence of microRNA on the maintenance of human iron metabolism. | 2013 Jul 10 |
4 |
| 52 |
23909240 | His86 from the N-terminus of frataxin coordinates iron and is required for Fe-S cluster synthesis. | 2013 Sep 3 |
4 |
| 53 |
22125086 | The defective splicing caused by the ISCU intron mutation in patients with myopathy with lactic acidosis is repressed by PTBP1 but can be derepressed by IGF2BP1. | 2012 Mar |
1 |
| 54 |
22155317 | Antisense oligonucleotide corrects splice abnormality in hereditary myopathy with lactic acidosis. | 2012 Feb 25 |
2 |
| 55 |
22896707 | Micromanaging Iron Homeostasis: hypoxia-inducible micro-RNA-210 suppresses iron homeostasis-related proteins. | 2012 Oct 5 |
1 |
| 56 |
23035118 | Tissue specificity of a human mitochondrial disease: differentiation-enhanced mis-splicing of the Fe-S scaffold gene ISCU renders patient cells more sensitive to oxidative stress in ISCU myopathy. | 2012 Nov 23 |
2 |
| 57 |
20957368 | Expression, purification, and characterization of an iron chaperon protein CyaY from Acidithiobacillus ferrooxidans. | 2011 Mar |
2 |
| 58 |
21298097 | Mammalian frataxin: an essential function for cellular viability through an interaction with a preformed ISCU/NFS1/ISD11 iron-sulfur assembly complex. | 2011 Jan 26 |
1 |
| 59 |
21499539 | Structural, Mechanistic and Coordination Chemistry of Relevance to the Biosynthesis of Iron-Sulfur and Related Iron Cofactors. | 2011 Apr 1 |
2 |
| 60 |
21671584 | Friedreich's ataxia variants I154F and W155R diminish frataxin-based activation of the iron-sulfur cluster assembly complex. | 2011 Jul 26 |
1 |
| 61 |
21801864 | miR-210 targets iron-sulfur cluster scaffold homologue in human trophoblast cell lines: siderosis of interstitial trophoblasts as a novel pathology of preterm preeclampsia and small-for-gestational-age pregnancies. | 2011 Aug |
2 |
| 62 |
21945528 | Functional characterization of Fdx1: evidence for an evolutionary relationship between P450-type and ISC-type ferredoxins. | 2011 Nov 11 |
1 |
| 63 |
21987576 | Specialized function of yeast Isa1 and Isa2 proteins in the maturation of mitochondrial [4Fe-4S] proteins. | 2011 Dec 2 |
1 |
| 64 |
20206689 | Differences in RNA processing underlie the tissue specific phenotype of ISCU myopathy. | 2010 Jun |
2 |
| 65 |
20404999 | Structural basis for Fe-S cluster assembly and tRNA thiolation mediated by IscS protein-protein interactions. | 2010 Apr 13 |
2 |
| 66 |
20436681 | MicroRNA-210 regulates mitochondrial free radical response to hypoxia and krebs cycle in cancer cells by targeting iron sulfur cluster protein ISCU. | 2010 Apr 26 |
3 |
| 67 |
20481466 | Human iron-sulfur cluster assembly, cellular iron homeostasis, and disease. | 2010 Jun 22 |
1 |
| 68 |
20873749 | Human frataxin is an allosteric switch that activates the Fe-S cluster biosynthetic complex. | 2010 Nov 2 |
1 |
| 69 |
20981023 | Structural bases for the interaction of frataxin with the central components of iron-sulphur cluster assembly. | 2010 Oct 19 |
1 |
| 70 |
19308466 | Iron-sulfur cluster biosynthesis: characterization of IscU-IscS complex formation and a structural model for sulfide delivery to the [2Fe-2S] assembly site. | 2009 Aug |
1 |
| 71 |
19462090 | Iron-sulfur cluster biosynthesis: role of a semi-conserved histidine. | 2009 Jun 7 |
1 |
| 72 |
19492851 | Structure and dynamics of the iron-sulfur cluster assembly scaffold protein IscU and its interaction with the cochaperone HscB. | 2009 Jul 7 |
2 |
| 73 |
19567699 | Clinical manifestation and a new ISCU mutation in iron-sulphur cluster deficiency myopathy. | 2009 Aug |
5 |
| 74 |
19846308 | Antisense oligonucleotide therapeutics for iron-sulphur cluster deficiency myopathy. | 2009 Dec |
1 |
| 75 |
18296749 | Myopathy with lactic acidosis is linked to chromosome 12q23.3-24.11 and caused by an intron mutation in the ISCU gene resulting in a splicing defect. | 2008 Jun 1 |
1 |
| 76 |
18304497 | Splice mutation in the iron-sulfur cluster scaffold protein ISCU causes myopathy with exercise intolerance. | 2008 Mar |
9 |
| 77 |
18606475 | Iron-sulfur cluster biogenesis and human disease. | 2008 Aug |
2 |
| 78 |
18986169 | Studies on the mechanism of catalysis of iron-sulfur cluster transfer from IscU[2Fe2S] by HscA/HscB chaperones. | 2008 Dec 2 |
5 |
| 79 |
17244611 | Distinct iron binding property of two putative iron donors for the iron-sulfur cluster assembly: IscA and the bacterial frataxin ortholog CyaY under physiological and oxidative stress conditions. | 2007 Mar 16 |
2 |
| 80 |
17331979 | Mitochondrial frataxin interacts with ISD11 of the NFS1/ISCU complex and multiple mitochondrial chaperones. | 2007 Apr 15 |
2 |
| 81 |
16517407 | Functions of mitochondrial ISCU and cytosolic ISCU in mammalian iron-sulfur cluster biogenesis and iron homeostasis. | 2006 Mar |
5 |
| 82 |
16527810 | Roles of the mammalian cytosolic cysteine desulfurase, ISCS, and scaffold protein, ISCU, in iron-sulfur cluster assembly. | 2006 May 5 |
3 |
| 83 |
16603772 | Iron-sulfur cluster biosynthesis: characterization of Escherichia coli CYaY as an iron donor for the assembly of [2Fe-2S] clusters in the scaffold IscU. | 2006 Jun 16 |
2 |
| 84 |
15766257 | Iron-sulfur cluster biosynthesis. Molecular chaperone DnaK promotes IscU-bound [2Fe-2S] cluster stability and inhibits cluster transfer activity. | 2005 Mar 22 |
6 |
| 85 |
15815978 | Structural characterization of an iron-sulfur cluster assembly protein IscU in a zinc-bound form. | 2005 Jun 1 |
1 |
| 86 |
15828873 | Mobilization of the iron centre in IscA for the iron-sulphur cluster assembly in IscU. | 2005 Aug 1 |
2 |
| 87 |
14720122 | Characterization of iron binding in IscA, an ancient iron-sulphur cluster assembly protein. | 2004 Apr 15 |
7 |
| 88 |
14993221 | Iron-sulfur cluster assembly: NifU-directed activation of the nitrogenase Fe protein. | 2004 May 7 |
1 |
| 89 |
15143178 | The yeast scaffold proteins Isu1p and Isu2p are required inside mitochondria for maturation of cytosolic Fe/S proteins. | 2004 Jun |
1 |
| 90 |
15247288 | IscA mediates iron delivery for assembly of iron-sulfur clusters in IscU under the limited accessible free iron conditions. | 2004 Sep 3 |
14 |
| 91 |
12756240 | Ssq1, a mitochondrial Hsp70 involved in iron-sulfur (Fe/S) center biogenesis. Similarities to and differences from its bacterial counterpart. | 2003 Aug 8 |
1 |
| 92 |
12886008 | Subcellular compartmentalization of human Nfu, an iron-sulfur cluster scaffold protein, and its ability to assemble a [4Fe-4S] cluster. | 2003 Aug 19 |
2 |
| 93 |
12137512 | Iron-sulfur cluster biosynthesis: characterization of iron nucleation sites for assembly of the [2Fe-2S]2+ cluster core in IscU proteins. | 2002 Jul 31 |
8 |
| 94 |
11686732 | Sulfur transfer from IscS to IscU: the first step in iron-sulfur cluster biosynthesis. | 2001 Nov 7 |
1 |
| 95 |
10891064 | IscU as a scaffold for iron-sulfur cluster biosynthesis: sequential assembly of [2Fe-2S] and [4Fe-4S] clusters in IscU. | 2000 Jul 11 |
4 |
| 96 |
11060020 | Distinct iron-sulfur cluster assembly complexes exist in the cytosol and mitochondria of human cells. | 2000 Nov 1 |
6 |
| 97 |
11123951 | Characterization of the NifU and NifS Fe-S cluster formation proteins essential for viability in Helicobacter pylori. | 2000 Dec 26 |
6 |