| 1 |
35314356 | Metal distribution in Cu/Zn-superoxide dismutase revealed by native mass spectrometry. | 2022 Apr |
3 |
| 2 |
33541434 | Protein disulfide isomerase ERp57 protects early muscle denervation in experimental ALS. | 2021 Feb 4 |
1 |
| 3 |
33923808 | A Metal-Free, Disulfide Oxidized Form of Superoxide Dismutase 1 as a Primary Misfolded Species with Prion-Like Properties in the Extracellular Environments Surrounding Motor Neuron-Like Cells. | 2021 Apr 16 |
2 |
| 4 |
34138531 | Ligand-Induced Stabilization of the Native Human Superoxide Dismutase 1. | 2021 Jul 7 |
1 |
| 5 |
31863908 | Oxidative misfolding of Cu/Zn-superoxide dismutase triggered by non-canonical intramolecular disulfide formation. | 2020 Feb 1 |
2 |
| 6 |
31931282 | Methylglyoxal interaction with superoxide dismutase 1. | 2020 Feb |
1 |
| 7 |
32056106 | Nucleation and kinetics of SOD1 aggregation in human cells for ALS1. | 2020 Mar |
1 |
| 8 |
32191862 | Friction-Limited Folding of Disulfide-Reduced Monomeric SOD1. | 2020 Apr 21 |
2 |
| 9 |
32768728 | Molecular dynamics of far positioned surface mutations of Cu/Zn SOD1 promotes altered structural stability and metal-binding site: Structural clues to the pathogenesis of amyotrophic lateral sclerosis. | 2020 Nov |
1 |
| 10 |
33679289 | A Novel SOD1 Intermediate Oligomer, Role of Free Thiols and Disulfide Exchange. | 2020 |
4 |
| 11 |
30635404 | CNS-derived extracellular vesicles from superoxide dismutase 1 (SOD1)G93A ALS mice originate from astrocytes and neurons and carry misfolded SOD1. | 2019 Mar 8 |
2 |
| 12 |
30863976 | The molecular pathogenesis of superoxide dismutase 1-linked ALS is promoted by low oxygen tension. | 2019 Jul |
2 |
| 13 |
31230748 | Far positioned ALS associated mutants of Cu/Zn SOD forms partially metallated, destabilized misfolding intermediates. | 2019 Aug 20 |
1 |
| 14 |
31292775 | Copper-zinc superoxide dismutase (Sod1) activation terminates interaction between its copper chaperone (Ccs) and the cytosolic metal-binding domain of the copper importer Ctr1. | 2019 Aug |
2 |
| 15 |
29220697 | Metabolism of hydrogen sulfide (H2S) and Production of Reactive Sulfur Species (RSS) by superoxide dismutase. | 2018 May |
2 |
| 16 |
29686043 | TFE-induced local unfolding and fibrillation of SOD1: bridging the experiment and simulation studies. | 2018 May 18 |
1 |
| 17 |
29869502 | In-Cell NMR in Human Cells: Direct Protein Expression Allows Structural Studies of Protein Folding and Maturation. | 2018 Jun 19 |
1 |
| 18 |
29950795 | Quantifying the Interaction between Copper-Zinc Superoxide Dismutase (Sod1) and its Copper Chaperone (Ccs1). | 2018 |
2 |
| 19 |
30038021 | Endoplasmic reticulum stress leads to accumulation of wild-type SOD1 aggregates associated with sporadic amyotrophic lateral sclerosis. | 2018 Aug 7 |
2 |
| 20 |
30429951 | Interaction of Half Oxa-/Half cis-Platin Complex with Human Superoxide Dismutase and Induced Reduction of Neurotoxicity. | 2018 Nov 8 |
1 |
| 21 |
28057013 | Immunochemical characterization on pathological oligomers of mutant Cu/Zn-superoxide dismutase in amyotrophic lateral sclerosis. | 2017 Jan 5 |
6 |
| 22 |
28533431 | Copper-zinc superoxide dismutase is activated through a sulfenic acid intermediate at a copper ion entry site. | 2017 Jul 21 |
6 |
| 23 |
28585802 | Cu/Zn Superoxide Dismutase Forms Amyloid Fibrils under Near-Physiological Quiescent Conditions: The Roles of Disulfide Bonds and Effects of Denaturant. | 2017 Sep 20 |
7 |
| 24 |
28629863 | The unfolding mechanism of monomeric mutant SOD1 by simulated force spectroscopy. | 2017 Nov |
1 |
| 25 |
28686251 | Oxygen-dependent activation of Cu,Zn-superoxide dismutase-1. | 2017 Aug 16 |
3 |
| 26 |
29234142 | A molecular chaperone activity of CCS restores the maturation of SOD1 fALS mutants. | 2017 Dec 12 |
2 |
| 27 |
26319711 | Structural basis of Cu, Zn-superoxide dismutase amyloid fibril formation involves interaction of multiple peptide core regions. | 2016 Feb |
3 |
| 28 |
26694608 | Conformational Disorder of the Most Immature Cu, Zn-Superoxide Dismutase Leading to Amyotrophic Lateral Sclerosis. | 2016 Feb 19 |
2 |
| 29 |
27261461 | Cellular Redox Systems Impact the Aggregation of Cu,Zn Superoxide Dismutase Linked to Familial Amyotrophic Lateral Sclerosis. | 2016 Aug 12 |
2 |
| 30 |
27378311 | SALS-linked WT-SOD1 adopts a highly similar helical conformation as FALS-causing L126Z-SOD1 in a membrane environment. | 2016 Sep |
1 |
| 31 |
27556028 | Screening of Drugs Inhibiting In vitro Oligomerization of Cu/Zn-Superoxide Dismutase with a Mutation Causing Amyotrophic Lateral Sclerosis. | 2016 |
1 |
| 32 |
27867347 | Susceptibility of Mutant SOD1 to Form a Destabilized Monomer Predicts Cellular Aggregation and Toxicity but Not In vitro Aggregation Propensity. | 2016 |
1 |
| 33 |
25306968 | Mechanism for transforming cytosolic SOD1 into integral membrane proteins of organelles by ALS-causing mutations. | 2015 Jan |
1 |
| 34 |
25433341 | Insights into the role of the unusual disulfide bond in copper-zinc superoxide dismutase. | 2015 Jan 23 |
5 |
| 35 |
25666897 | Curcumin binds to the pre-fibrillar aggregates of Cu/Zn superoxide dismutase (SOD1) and alters its amyloidogenic pathway resulting in reduced cytotoxicity. | 2015 May |
2 |
| 36 |
25938783 | Prevention of PKG1α oxidation augments cardioprotection in the stressed heart. | 2015 Jun |
1 |
| 37 |
26207449 | Voltage-Induced Misfolding of Zinc-Replete ALS Mutant Superoxide Dismutase-1. | 2015 Oct 21 |
2 |
| 38 |
26511321 | The Disulfide Bond, but Not Zinc or Dimerization, Controls Initiation and Seeded Growth in Amyotrophic Lateral Sclerosis-linked Cu,Zn Superoxide Dismutase (SOD1) Fibrillation. | 2015 Dec 18 |
7 |
| 39 |
24793051 | Study on the disulfide bond and disulfide loop of native and mutated SOD1 protein. | 2014 May |
3 |
| 40 |
24968724 | Structural insights of proteins in sub-cellular compartments: In-mitochondria NMR. | 2014 Nov |
2 |
| 41 |
25096579 | Altered thiol chemistry in human amyotrophic lateral sclerosis-linked mutants of superoxide dismutase 1. | 2014 Sep 26 |
8 |
| 42 |
22867017 | Disulfide bond as a switch for copper-zinc superoxide dismutase activity in asthma. | 2013 Feb 1 |
1 |
| 43 |
23076707 | Composition of soluble misfolded superoxide dismutase-1 in murine models of amyotrophic lateral sclerosis. | 2013 Mar |
1 |
| 44 |
23264618 | Disulfide scrambling describes the oligomer formation of superoxide dismutase (SOD1) proteins in the familial form of amyotrophic lateral sclerosis. | 2013 Feb 15 |
12 |
| 45 |
23291526 | Mechanical probes of SOD1 predict systematic trends in metal and dimer affinity of ALS-associated mutants. | 2013 Mar 11 |
2 |
| 46 |
23455544 | Atomic-resolution monitoring of protein maturation in live human cells by NMR. | 2013 May |
2 |
| 47 |
23625804 | Mechanistic aspects of hSOD1 maturation from the solution structure of Cu(I) -loaded hCCS domain 1 and analysis of disulfide-free hSOD1 mutants. | 2013 Sep 23 |
1 |
| 48 |
23780345 | A structural modeling approach for the understanding of initiation and elongation of ALS-linked superoxide dismutase fibrils. | 2013 Sep |
3 |
| 49 |
23802566 | Mia40 and MINOS act in parallel with Ccs1 in the biogenesis of mitochondrial Sod1. | 2013 Oct |
1 |
| 50 |
24143259 | Disulfide scrambling in superoxide dismutase 1 reduces its cytotoxic effect in cultured cells and promotes protein aggregation. | 2013 |
2 |