| 1 |
35157847 | Deglutarylation of glutaryl-CoA dehydrogenase by deacylating enzyme SIRT5 promotes lysine oxidation in mice. | 2022 Apr |
9 |
| 2 |
29779173 | Long Lasting High Lysine Diet Aggravates White Matter Injury in Glutaryl-CoA Dehydrogenase Deficient (Gcdh-/-) Mice. | 2019 Jan |
4 |
| 3 |
31125684 | Pathogenesis of brain damage in glutaric acidemia type I: Lessons from the genetic mice model. | 2019 Nov |
4 |
| 4 |
28545977 | Elevated glutaric acid levels in Dhtkd1-/Gcdh- double knockout mice challenge our current understanding of lysine metabolism. | 2017 Sep |
1 |
| 5 |
26607633 | Oxidative Stress, Disrupted Energy Metabolism, and Altered Signaling Pathways in Glutaryl-CoA Dehydrogenase Knockout Mice: Potential Implications of Quinolinic Acid Toxicity in the Neuropathology of Glutaric Acidemia Type I. | 2016 Nov |
1 |
| 6 |
25558815 | Multifactorial modulation of susceptibility to l-lysine in an animal model of glutaric aciduria type I. | 2015 May |
1 |
| 7 |
25968119 | Striatal neuronal death mediated by astrocytes from the Gcdh-/- mouse model of glutaric acidemia type I. | 2015 Aug 15 |
3 |
| 8 |
26671102 | Experimental evidence that overexpression of NR2B glutamate receptor subunit is associated with brain vacuolation in adult glutaryl-CoA dehydrogenase deficient mice: A potential role for glutamatergic-induced excitotoxicity in GA I neuropathology. | 2015 Dec 15 |
1 |
| 9 |
24594605 | Increased glutamate receptor and transporter expression in the cerebral cortex and striatum of gcdh-/- mice: possible implications for the neuropathology of glutaric acidemia type I. | 2014 |
1 |
| 10 |
24996493 | Acute lysine overload provokes protein oxidative damage and reduction of antioxidant defenses in the brain of infant glutaryl-CoA dehydrogenase deficient mice: a role for oxidative stress in GA I neuropathology. | 2014 Sep 15 |
1 |
| 11 |
23218171 | Disruption of brain redox homeostasis in glutaryl-CoA dehydrogenase deficient mice treated with high dietary lysine supplementation. | 2013 Jan |
1 |
| 12 |
22445450 | Induction of oxidative stress in brain of glutaryl-CoA dehydrogenase deficient mice by acute lysine administration. | 2012 May |
3 |
| 13 |
22578804 | Marked reduction of Na(+), K(+)-ATPase and creatine kinase activities induced by acute lysine administration in glutaryl-CoA dehydrogenase deficient mice. | 2012 Sep |
2 |
| 14 |
20923787 | Therapeutic modulation of cerebral L-lysine metabolism in a mouse model for glutaric aciduria type I. | 2011 Jan |
2 |
| 15 |
16446282 | A diet-induced mouse model for glutaric aciduria type I. | 2006 Apr |
4 |