| 51 |
20335223 | The mutation N528S in the von Willebrand factor (VWF) propeptide causes defective multimerization and storage of VWF. | 2010 Jun 3 |
5 |
| 52 |
20403097 | Functional variation in the arginine vasopressin 2 receptor as a modifier of human plasma von Willebrand factor levels. | 2010 Jul |
3 |
| 53 |
20590859 | von Willebrand's disease diagnosis and laboratory issues. | 2010 Jul |
1 |
| 54 |
19192112 | Genetic alteration of the D2 domain abolishes von Willebrand factor multimerization and trafficking into storage. | 2009 Apr |
3 |
| 55 |
19308894 | Toward a new paradigm for the identification and functional characterization of von Willebrand disease. | 2009 Feb |
1 |
| 56 |
19506357 | Laboratory and molecular characteristics of recessive von Willebrand disease type 2C (2A subtype IIC) of variable severity due to homozygous or double heterozygous mutations in the D1 and D2 domains. | 2009 |
2 |
| 57 |
19506359 | Laboratory diagnosis of von Willebrand disease type 1/2E (2A subtype IIE), type 1 Vicenza and mild type 1 caused by mutations in the D3, D4, B1-B3 and C1-C2 domains of the von Willebrand factor gene. Role of von Willebrand factor multimers and the von Willebrand factor propeptide/antigen ratio. | 2009 |
1 |
| 58 |
19578117 | Molecular requirements for sorting of the chemokine interleukin-8/CXCL8 to endothelial Weibel-Palade bodies. | 2009 Aug 28 |
2 |
| 59 |
19707594 | Models for prediction of factor VIII half-life in severe haemophiliacs: distinct approaches for blood group O and non-O patients. | 2009 Aug 25 |
2 |
| 60 |
17949477 | von Willebrand factor: evidence for variable clearance in vivo according to Y/C1584 phenotype and ABO blood group. | 2008 Jan |
1 |
| 61 |
18245665 | A shorter von Willebrand factor survival in O blood group subjects explains how ABO determinants influence plasma von Willebrand factor. | 2008 Apr 1 |
3 |
| 62 |
18328061 | Expression studies of missense mutations p.D141Y, p.C275S located in the propeptide of von Willebrand factor in patients with type 3 von Willebrand disease. | 2008 May |
1 |
| 63 |
18344424 | Identification of type 1 von Willebrand disease patients with reduced von Willebrand factor survival by assay of the VWF propeptide in the European study: molecular and clinical markers for the diagnosis and management of type 1 VWD (MCMDM-1VWD). | 2008 May 15 |
4 |
| 64 |
18690339 | Characterization of a novel mutation in the von Willebrand factor propeptide in a distinct subtype of recessive von Willebrand disease. | 2008 Aug |
1 |
| 65 |
18691167 | Von Willebrand factor propeptide makes it easy to identify the shorter Von Willebrand factor survival in patients with type 1 and type Vicenza von Willebrand disease. | 2008 Oct |
4 |
| 66 |
17090649 | Variations in glycosylation of von Willebrand factor with O-linked sialylated T antigen are associated with its plasma levels. | 2007 Mar 15 |
1 |
| 67 |
17200766 | Relatively increased von Willebrand factor activity after off-pump coronary artery bypass graft surgery. | 2007 Jan |
1 |
| 68 |
17456630 | Identifying carriers of type 2N von Willebrand disease: procedures and significance. | 2007 Apr |
1 |
| 69 |
17764538 | ADAMTS-13, von Willebrand factor and related parameters in severe sepsis and septic shock. | 2007 Nov |
1 |
| 70 |
17895385 | Two Cys residues essential for von Willebrand factor multimer assembly in the Golgi. | 2007 Oct 2 |
1 |
| 71 |
16459301 | The physiological function of von Willebrand's factor depends on its tubular storage in endothelial Weibel-Palade bodies. | 2006 Feb |
1 |
| 72 |
16681646 | von Willebrand factor propeptide in malaria: evidence of acute endothelial cell activation. | 2006 Jun |
5 |
| 73 |
16835381 | Assay of the von Willebrand factor (VWF) propeptide to identify patients with type 1 von Willebrand disease with decreased VWF survival. | 2006 Nov 15 |
4 |
| 74 |
16953269 | Type 2N von Willebrand disease due to compound heterozygosity for R854Q and a novel R763G mutation at the cleavage site of von Willebrand factor propeptide. | 2006 Sep |
3 |
| 75 |
16968329 | Acute activation of the endothelium results in increased levels of active von Willebrand factor in hemolysis, elevated liver enzymes and low platelets (HELLP) syndrome. | 2006 Dec |
1 |
| 76 |
17059421 | von Willebrand factor and its propeptide: the influence of secretion and clearance on protein levels and the risk of venous thrombosis. | 2006 Dec |
10 |
| 77 |
17139363 | Combined partial exon skipping and cryptic splice site activation as a new molecular mechanism for recessive type 1 von Willebrand disease. | 2006 Dec |
2 |
| 78 |
16102036 | von Willebrand factor: two sides of a coin. | 2005 Aug |
1 |
| 79 |
14690496 | How to roll an endothelial cigar: the biogenesis of Weibel-Palade bodies. | 2004 Feb |
1 |
| 80 |
12393513 | Critical independent regions in the VWF propeptide and mature VWF that enable normal VWF storage. | 2003 Feb 15 |
3 |
| 81 |
12393698 | An Arg760Cys mutation in the consensus sequence of the von Willebrand factor propeptide cleavage site is responsible for a new von Willebrand disease variant. | 2003 Jan 1 |
8 |
| 82 |
12393734 | Changes in von Willebrand factor-cleaving protease (ADAMTS13) activity after infusion of desmopressin. | 2003 Feb 1 |
1 |
| 83 |
12595584 | von Willebrand factor and its propeptide in children with diabetes. Relation between endothelial dysfunction and microalbuminuria. | 2003 Mar |
2 |
| 84 |
12618268 | Differential intracellular trafficking of von Willebrand factor (vWF) and vWF propeptide in porcine endothelial cells lacking Weibel-Palade bodies and in human endothelial cells. | 2003 Mar |
1 |
| 85 |
12786801 | Reassessment of von Willebrand factor (VWF), VWF propeptide, factor VIII:C and plasminogen activator inhibitors 1 and 2 during normal pregnancy. | 2003 Jun |
1 |
| 86 |
14526622 | [Acquired von Willebrand syndrome]. | 2003 Sep 13 |
1 |
| 87 |
12176890 | The role of the D1 domain of the von Willebrand factor propeptide in multimerization of VWF. | 2002 Sep 1 |
3 |
| 88 |
11299058 | Von Willebrand factor propeptide as a marker of disease activity in systemic sclerosis (scleroderma). | 2001 |
1 |
| 89 |
11487004 | Von Willebrand factor propeptide in vascular disorders. | 2001 Jul |
1 |
| 90 |
11686098 | Biosynthesis, processing and secretion of von Willebrand factor: biological implications. | 2001 Jun |
2 |
| 91 |
11776313 | Thrombin-mediated in vitro processing of pro-von Willebrand factor. | 2001 Dec |
2 |
| 92 |
10896250 | Platelets release thrombopoietin (Tpo) upon activation: another regulatory loop in thrombocytopoiesis? | 2000 Jun |
1 |
| 93 |
10961880 | von Willebrand factor storage and multimerization: 2 independent intracellular processes. | 2000 Sep 1 |
2 |
| 94 |
10381511 | von Willebrand factor propeptide in vascular disorders: A tool to distinguish between acute and chronic endothelial cell perturbation. | 1999 Jul 1 |
3 |
| 95 |
9569179 | Ins405AsnPro mutation in the von Willebrand factor propeptide in recessive type 2A (IIC) von Willebrand's disease. | 1998 Apr |
4 |
| 96 |
9657753 | Binding of factor VIII to von willebrand factor is enabled by cleavage of the von Willebrand factor propeptide and enhanced by formation of disulfide-linked multimers. | 1998 Jul 15 |
21 |
| 97 |
9684782 | Comparison between von Willebrand factor (VWF) and VWF antigen II in normal individuals and patients with von Willebrand disease. | 1998 Jul |
1 |
| 98 |
9714529 | A new candidate mutation (N528S) within the von Willebrand factor propeptide identified in a Japanese patient with phenotype IIC of von Willebrand disease. | 1998 Aug |
4 |
| 99 |
9759633 | Quantitative analysis of von Willebrand factor and its propeptide in plasma in acquired von Willebrand syndrome. | 1998 Sep |
4 |
| 100 |
9869174 | von Willebrand factor (vWf) as a plasma marker of endothelial activation in diabetes: improved reliability with parallel determination of the vWf propeptide (vWf:AgII). | 1998 Dec |
4 |