| 1 |
33521459 | Heme-Thiolate Perturbation in Cystathionine β-Synthase by Mercury Compounds. | 2021 Jan 26 |
2 |
| 2 |
34495791 | Understanding the role of R266K mutation in cystathionine β-synthase (CBS) enzyme: an in silico study. | 2021 Sep 8 |
4 |
| 3 |
31857119 | Classical homocystinuria: From cystathionine beta-synthase deficiency to novel enzyme therapies. | 2020 Jun |
1 |
| 4 |
32487371 | Hyperhomocysteinemia in patients with acute porphyrias: A potentially dangerous metabolic crossroad? | 2020 Sep |
2 |
| 5 |
31893496 | Hydrogen sulfide formation in experimental model of acute pancreatitis. | 2019 Dec 27 |
2 |
| 6 |
30393252 | [Production of H2S, H2Sn, and persulfide species (CysSSH and GSSH) by 3-mercaptopyruvate sulfurtransferase]. | 2018 |
1 |
| 7 |
28421128 | A Clinically Relevant Variant of the Human Hydrogen Sulfide-Synthesizing Enzyme Cystathionine β-Synthase: Increased CO Reactivity as a Novel Molecular Mechanism of Pathogenicity? | 2017 |
2 |
| 8 |
26867575 | Kinetics of Nitrite Reduction and Peroxynitrite Formation by Ferrous Heme in Human Cystathionine β-Synthase. | 2016 Apr 8 |
1 |
| 9 |
26962179 | Short-Term Vitamin B-6 Restriction Does Not Affect Plasma Concentrations of Hydrogen Sulfide Biomarkers Lanthionine and Homolanthionine in Healthy Men and Women. | 2015 Apr 1 |
1 |
| 10 |
24598918 | Purification, crystallization and preliminary crystallographic analysis of the catalytic core of cystathionine β-synthase from Saccharomyces cerevisiae. | 2014 Mar |
2 |
| 11 |
23002992 | Comparative study of enzyme activity and heme reactivity in Drosophila melanogaster and Homo sapiens cystathionine β-synthases. | 2013 Jan 29 |
2 |
| 12 |
23790103 | Kinetics of reversible reductive carbonylation of heme in human cystathionine β-synthase. | 2013 Jul 2 |
1 |
| 13 |
24043838 | Structural basis of regulation and oligomerization of human cystathionine β-synthase, the central enzyme of transsulfuration. | 2013 Oct 1 |
1 |
| 14 |
22333527 | Folding and activity of mutant cystathionine β-synthase depends on the position and nature of the purification tag: characterization of the R266K CBS mutant. | 2012 Apr |
2 |
| 15 |
22738154 | Effect of the disease-causing R266K mutation on the heme and PLP environments of human cystathionine β-synthase. | 2012 Aug 14 |
5 |
| 16 |
23124209 | Detection of reaction intermediates during human cystathionine β-synthase-monitored turnover and H2S production. | 2012 Dec 21 |
3 |
| 17 |
20821054 | Determination of cystathionine beta-synthase activity in human plasma by LC-MS/MS: potential use in diagnosis of CBS deficiency. | 2011 Feb |
3 |
| 18 |
21262193 | Purification and characterization of cystathionine β-synthase bearing a cobalt protoporphyrin. | 2011 Apr 1 |
2 |
| 19 |
21275900 | Hydrogen sulfide generation in mammals: the molecular biology of cystathionine-β- synthase (CBS) and cystathionine-γ-lyase (CSE). | 2011 Apr |
4 |
| 20 |
21480614 | Cobalt cystathionine β-synthase: a cobalt-substituted heme protein with a unique thiolate ligation motif. | 2011 May 16 |
2 |
| 21 |
20155941 | Investigations of low-frequency vibrational dynamics and ligand binding kinetics of cystathionine beta-synthase. | 2010 Mar 11 |
1 |
| 22 |
19019829 | Structural basis for the inhibition mechanism of human cystathionine gamma-lyase, an enzyme responsible for the production of H(2)S. | 2009 Jan 30 |
1 |
| 23 |
19232736 | Modulation of the heme electronic structure and cystathionine beta-synthase activity by second coordination sphere ligands: The role of heme ligand switching in redox regulation. | 2009 May |
2 |
| 24 |
19733148 | Inactivation of cystathionine beta-synthase with peroxynitrite. | 2009 Nov |
2 |
| 25 |
18278872 | Dioxygen reactivity and heme redox potential of truncated human cystathionine beta-synthase. | 2008 Mar 11 |
1 |
| 26 |
17377202 | Hydrogen sulfide (H2S) - the third gas of interest for pharmacologists. | 2007 Jan-Feb |
1 |
| 27 |
17956124 | Ferrous human cystathionine beta-synthase loses activity during enzyme assay due to a ligand switch process. | 2007 Nov 13 |
2 |
| 28 |
16505479 | Dynamics of carbon monoxide binding to cystathionine beta-synthase. | 2006 May 12 |
2 |
| 29 |
17069888 | Structural insights into pathogenic mutations in heme-dependent cystathionine-beta-synthase. | 2006 Dec |
1 |
| 30 |
15196993 | Visualization of PLP-bound intermediates in hemeless variants of human cystathionine beta-synthase: evidence that lysine 119 is a general base. | 2004 Jul 15 |
2 |
| 31 |
15280798 | [Hydrogen sulfide as a biologically active mediator in the cardiovascular system]. | 2004 Jul 19 |
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| 32 |
15544339 | The redox behavior of the heme in cystathionine beta-synthase is sensitive to pH. | 2004 Nov 23 |
2 |
| 33 |
15642325 | The presence of a transsulfuration pathway in the lens: a new oxidative stress defense system. | 2004 Dec |
1 |
| 34 |
12686134 | Structural insights into mutations of cystathionine beta-synthase. | 2003 Apr 11 |
4 |
| 35 |
11926827 | Effects of heme ligand mutations including a pathogenic variant, H65R, on the properties of human cystathionine beta-synthase. | 2002 Apr 9 |
2 |
| 36 |
12173932 | Human cystathionine beta-synthase is a heme sensor protein. Evidence that the redox sensor is heme and not the vicinal cysteines in the CXXC motif seen in the crystal structure of the truncated enzyme. | 2002 Aug 20 |
1 |
| 37 |
12269827 | Alleviation of intrasteric inhibition by the pathogenic activation domain mutation, D444N, in human cystathionine beta-synthase. | 2002 Oct 1 |
1 |
| 38 |
12379655 | Deletion mutagenesis of human cystathionine beta-synthase. Impact on activity, oligomeric status, and S-adenosylmethionine regulation. | 2002 Dec 13 |
1 |
| 39 |
11042162 | Functional properties of the active core of human cystathionine beta-synthase crystals. | 2001 Jan 5 |
1 |
| 40 |
11483494 | Structure of human cystathionine beta-synthase: a unique pyridoxal 5'-phosphate-dependent heme protein. | 2001 Aug 1 |
3 |
| 41 |
11744063 | Mercuric chloride-induced spin or ligation state changes in ferric or ferrous human cystathionine beta-synthase inhibit enzyme activity. | 2001 Dec 15 |
1 |
| 42 |
10052944 | Characterization of the heme and pyridoxal phosphate cofactors of human cystathionine beta-synthase reveals nonequivalent active sites. | 1999 Mar 2 |
2 |
| 43 |
10353853 | Characterization of the heme and pyridoxal phosphate cofactors of human cystathionine beta-synthase reveals nonequivalent active sites | 1999 Jun 1 |
1 |
| 44 |
10444346 | Relation between plasma homocysteine concentration, the 844ins68 variant of the cystathionine beta-synthase gene, and pyridoxal-5'-phosphate concentration. | 1999 Aug |
3 |
| 45 |
10529187 | Assignment of enzymatic functions to specific regions of the PLP-dependent heme protein cystathionine beta-synthase. | 1999 Oct 5 |
1 |
| 46 |
10531322 | Deletion of the regulatory domain in the pyridoxal phosphate-dependent heme protein cystathionine beta-synthase alleviates the defect observed in a catalytic site mutant. | 1999 Oct 29 |
1 |
| 47 |
10609891 | Vitamin B6 enzymes participating in selenium amino acid metabolism. | 1999 |
1 |
| 48 |
7840623 | Delta-aminolevulinate increases heme saturation and yield of human cystathionine beta-synthase expressed in Escherichia coli. | 1995 Jan 10 |
1 |
| 49 |
7967489 | Komrower Lecture. Molecular basis of phenotype expression in homocystinuria. | 1994 |
1 |
| 50 |
8507876 | Elevation of serum cystathionine levels in patients with cobalamin and folate deficiency. | 1993 Jun 15 |
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