Glycosaminoglycans

iduronate 2-sulfatase ; Mus musculus







18 Article(s)
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1 35284671 Iduronate-2-sulfatase interactome: validation by yeast two-hybrid assay. 2022 Mar 2
2 34622797 Iduronate-2-sulfatase transport vehicle rescues behavioral and skeletal phenotypes in a mouse model of Hunter syndrome. 2021 Oct 8 2
3 32631737 Efficient engraftment of genetically modified cells is necessary to ameliorate central nervous system involvement of murine model of mucopolysaccharidosis type II by hematopoietic stem cell targeted gene therapy. 2020 Aug 1
4 32751752 High-Throughput Liquid Chromatography-Tandem Mass Spectrometry Quantification of Glycosaminoglycans as Biomarkers of Mucopolysaccharidosis II. 2020 Jul 30 2
5 31193135 Identification of the iduronate-2-sulfatase proteome in wild-type mouse brain. 2019 May 2
6 29606503 A Blood-Brain-Barrier-Penetrating Anti-human Transferrin Receptor Antibody Fusion Protein for Neuronopathic Mucopolysaccharidosis II. 2018 May 2 1
7 29978271 The efficacy of intracerebroventricular idursulfase-beta enzyme replacement therapy in mucopolysaccharidosis II murine model: heparan sulfate in cerebrospinal fluid as a clinical biomarker of neuropathology. 2018 Nov 2
8 30064964 Evaluation of cerebrospinal fluid heparan sulfate as a biomarker of neuropathology in a murine model of mucopolysaccharidosis type II using high-sensitivity LC/MS/MS. 2018 Sep 1
9 28478695 Prevention of Neurocognitive Deficiency in Mucopolysaccharidosis Type II Mice by Central Nervous System-Directed, AAV9-Mediated Iduronate Sulfatase Gene Transfer. 2017 Aug 1
10 27699273 CNS-directed gene therapy for the treatment of neurologic and somatic mucopolysaccharidosis type II (Hunter syndrome). 2016 Jun 16 2
11 25761450 Hematopoietic Stem Cell Gene Therapy Corrects Neuropathic Phenotype in Murine Model of Mucopolysaccharidosis Type II. 2015 Jun 1
12 23529876 Improvement of CNS defects via continuous intrathecal enzyme replacement by osmotic pump in mucopolysaccharidosis type II mice. 2013 May 2
13 22279584 CNS penetration of intrathecal-lumbar idursulfase in the monkey, dog and mouse: implications for neurological outcomes of lysosomal storage disorder. 2012 1
14 22704483 Enzyme replacement therapy (ERT) procedure for mucopolysaccharidosis type II (MPS II) by intraventricular administration (IVA) in murine MPS II. 2012 Sep 1
15 21319344 Changes in glycogen and glycosaminoglycan levels in hepatocytes of iduronate-2-sulfatase knockout mice before and after recombinant iduronate-2-sulfatase supplementation. 2011 Mar 1
16 17459751 Preclinical dose ranging studies for enzyme replacement therapy with idursulfase in a knock-out mouse model of MPS II. 2007 Jun 4
17 15966019 Reduction of GAG storage in MPS II mouse model following implantation of encapsulated recombinant myoblasts. 2005 Nov 4
18 8325651 Cloning and characterization of the cDNA for the murine iduronate sulfatase gene. 1993 Jun 1