Heparitin Sulfate

alpha-N-acetylglucosaminidase (Sanfilippo disease IIIB) ; Mus musculus







16 Article(s)
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Title
Pub. Year
#Total Relationships
1 33839004 Biochemical evaluation of intracerebroventricular rhNAGLU-IGF2 enzyme replacement therapy in neonatal mice with Sanfilippo B syndrome. 2021 Jun 2
2 32111039 Proteomic Analysis of Mucopolysaccharidosis IIIB Mouse Brain. 2020 Feb 26 2
3 29186350 Macrophage enzyme and reduced inflammation drive brain correction of mucopolysaccharidosis IIIB by stem cell gene therapy. 2018 Jan 1 2
4 30101150 Genetically Corrected iPSC-Derived Neural Stem Cell Grafts Deliver Enzyme Replacement to Affect CNS Disease in Sanfilippo B Mice. 2018 Sep 21 1
5 28664165 Clearance of Heparan Sulfate and Attenuation of CNS Pathology by Intracerebroventricular BMN 250 in Sanfilippo Type B Mice. 2017 Sep 15 4
6 27064211 Identification of an anti-sperm auto-monoclonal antibody (Ts4)-recognized molecule in the mouse sperm acrosomal region and its inhibitory effect on fertilization in vitro. 2016 Jun 2
7 25332157 Oxidative stress is independent of inflammation in the neurodegenerative Sanfilippo syndrome type B. 2015 Mar 2
8 26147524 The Murine Model of Mucopolysaccharidosis IIIB Develops Cardiopathies over Time Leading to Heart Failure. 2015 4
9 25267636 Delivery of an enzyme-IGFII fusion protein to the mouse brain is therapeutic for mucopolysaccharidosis type IIIB. 2014 Oct 14 1
10 22867887 Accelerated clinical disease and pathology in mucopolysaccharidosis type IIIB and GalNAc transferase double knockout mice. 2012 Sep 4
11 21408219 Blood-brain barrier impairment in an animal model of MPS III B. 2011 Mar 7 1
12 21618584 Activation of stress kinases in the brain of mucopolysaccharidosis IIIB mice. 2011 Sep 2
13 19399896 Intravenous administration of human umbilical cord blood cells in an animal model of MPS III B. 2009 Jul 1 4
14 17185018 Lysosomal accumulation of SCMAS (subunit c of mitochondrial ATP synthase) in neurons of the mouse model of mucopolysaccharidosis III B. 2007 Apr 1
15 14727810 Mouse model of Sanfilippo syndrome type B: relation of phenotypic features to background strain. 2003 Dec 2
16 10588735 Mouse model of Sanfilippo syndrome type B produced by targeted disruption of the gene encoding alpha-N-acetylglucosaminidase. 1999 Dec 7 2