Fatty Acids

acyl-CoA dehydrogenase very long chain ; Homo sapiens







36 Article(s)
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1 34437764 Altered mitochondrial metabolism in peripheral blood cells from patients with inborn errors of ╬▓-oxidation. 2022 Jan 1
2 35001339 VLCAD inhibits the proliferation and invasion of hepatocellular cancer cells through regulating PI3K/AKT axis. 2022 May 2
3 33725513 Mitochondrial morphology, bioenergetics and proteomic responses in fatty acid oxidation disorders. 2021 May 2
4 34245263 Fetal Cardiac Lipid Sensing Triggers an Early and Sex-related Metabolic Energy Switch in Intrauterine Growth Restriction. 2021 Oct 21 1
5 34465376 A novel mutation in ACADVL causing very long-chain acyl-coenzyme-A dehydrogenase deficiency in a South Asian pediatric patient: a case report and review of the literature. 2021 Sep 1 1
6 34740033 Alterations in hepatic fatty acids reveal depletion of total polyunsaturated fatty acids following irinotecan plus 5-fluorouracil treatment in an animal model of colorectal cancer. 2021 Nov 1
7 32669490 Adult-onset Repeat Rhabdomyolysis with a Very Long-chain Acyl-CoA Dehydrogenase Deficiency Due to Compound Heterozygous ACADVL Mutations. 2020 Nov 1 2
8 33597881 Electrophysiological Abnormalities in VLCAD Deficient hiPSC-Cardiomyocytes Do not Improve with Carnitine Supplementation. 2020 1
9 30401918 Management and diagnosis of mitochondrial fatty acid oxidation disorders: focus on very-long-chain acyl-CoA dehydrogenase deficiency. 2019 Feb 2
10 28980192 Clinical, Biochemical, and Molecular Features in 37 Saudi Patients with Very Long Chain Acyl CoA Dehydrogenase Deficiency. 2018 1
11 29459657 Very long-/ and long Chain-3-Hydroxy Acyl CoA Dehydrogenase Deficiency correlates with deregulation of the mitochondrial fusion/fission machinery. 2018 Feb 19 1
12 29499131 Dynamic Regulation of Long-Chain Fatty Acid Oxidation by a Noncanonical Interaction between the MCL-1 BH3 Helix and VLCAD. 2018 Mar 1 2
13 27076444 The Regulation of Fatty Acid Oxidation in Human Preeclampsia. 2016 Oct 2
14 27644403 Activation of PPAR╬▒ by Fatty Acid Accumulation Enhances Fatty Acid Degradation and Sulfatide Synthesis. 2016 Oct 2
15 25737446 Strategies for correcting very long chain acyl-CoA dehydrogenase deficiency. 2015 Apr 17 1
16 25811481 SIRT3 and SIRT5 regulate the enzyme activity and cardiolipin binding of very long-chain acyl-CoA dehydrogenase. 2015 3
17 25843429 A heterozygous missense mutation in adolescent-onset very long-chain acyl-CoA dehydrogenase deficiency with exercise-induced rhabdomyolysis. 2015 Apr 1
18 26051273 Nickel inhibits mitochondrial fatty acid oxidation. 2015 Aug 7 2
19 26147000 Energy Metabolism Disorder as a Contributing Factor of Rheumatoid Arthritis: A Comparative Proteomic and Metabolomic Study. 2015 1
20 23185754 [Study on gene differential expressions of substance and energy metabolism in chronic superficial gastritis patients of Pi deficiency syndrome and of pi-wei hygropyrexia syndrome]. 2012 Sep 1
21 22093833 Role of suppressor of cytokine signaling 3 in lipid metabolism: analysis based on a phage-display human liver cDNA library. 2011 Dec 9 3
22 19889959 Dysregulation of very long chain acyl-CoA dehydrogenase coupled with lipid peroxidation. 2010 Jan 1
23 20480395 High-resolution melting analysis, a simple and effective method for reliable mutation scanning and frequency studies in the ACADVL gene. 2010 Jun 1
24 20816094 Acyl-CoA dehydrogenase 9 is required for the biogenesis of oxidative phosphorylation complex I. 2010 Sep 8 1
25 19156135 Biochemical correction of very long-chain acyl-CoA dehydrogenase deficiency following adeno-associated virus gene therapy. 2009 Mar 1
26 19535822 An overview of beta-oxidation disorders. 2009 Jun 8 1
27 19649258 A novel tandem mass spectrometry method for rapid confirmation of medium- and very long-chain acyl-CoA dehydrogenase deficiency in newborns. 2009 Jul 30 1
28 17374501 Expression and characterization of mutations in human very long-chain acyl-CoA dehydrogenase using a prokaryotic system. 2007 Jun 2
29 11524729 Mutation analysis in mitochondrial fatty acid oxidation defects: Exemplified by acyl-CoA dehydrogenase deficiencies, with special focus on genotype-phenotype relationship. 2001 Sep 2
30 10700700 Death caused by perioperative fasting and sedation in a child with unrecognized very long chain acyl-coenzyme A dehydrogenase deficiency. 2000 Mar 1
31 9973285 Clear correlation of genotype with disease phenotype in very-long-chain acyl-CoA dehydrogenase deficiency. 1999 Feb 2
32 10077518 Molecular heterogeneity in very-long-chain acyl-CoA dehydrogenase deficiency causing pediatric cardiomyopathy and sudden death. 1999 Mar 16 2
33 10607478 Characterization of the human very-long-chain acyl-CoA dehydrogenase gene promoter region: a role for activator protein 2. 1999 Dec 2
34 9498103 Mitochondrial very-long-chain acyl-coenzyme A dehydrogenase deficiency: clinical characteristics and diagnostic considerations in 30 patients. 1998 Jan 12 2
35 8650121 Prenatal diagnosis of mitochondrial fatty acid oxidation defects. 1996 Feb 2
36 8845838 Cloning and characterization of human very-long-chain acyl-CoA dehydrogenase cDNA, chromosomal assignment of the gene and identification in four patients of nine different mutations within the VLCAD gene. 1996 Apr 2