| 1 |
35269829 | CFTR, Cell Junctions and the Cytoskeleton. | 2022 Feb 28 |
1 |
| 2 |
35453033 | Overview of CF lung pathophysiology. | 2022 Jun |
2 |
| 3 |
35462606 | Downregulation of epithelial sodium channel (ENaC) activity in cystic fibrosis cells by epigenetic targeting. | 2022 Apr 25 |
2 |
| 4 |
33434105 | SARS-CoV-2 may hijack GPCR signaling pathways to dysregulate lung ion and fluid transport. | 2021 Mar 1 |
2 |
| 5 |
33916525 | DNA Methylation Patterns Correlate with the Expression of SCNN1A, SCNN1B, and SCNN1G (Epithelial Sodium Channel, ENaC) Genes. | 2021 Apr 4 |
1 |
| 6 |
34037494 | Association of cystic fibrosis transmembrane conductance regulator with epithelial sodium channel subunits carrying Liddle's syndrome mutations. | 2021 Aug 1 |
2 |
| 7 |
34831067 | CFTR Protein: Not Just a Chloride Channel? | 2021 Oct 22 |
1 |
| 8 |
32178452 | Measurement of Multi Ion Transport through Human Bronchial Epithelial Cell Line Provides an Insight into the Mechanism of Defective Water Transport in Cystic Fibrosis. | 2020 Mar 12 |
1 |
| 9 |
32606316 | COVID-19 meets Cystic Fibrosis: for better or worse? | 2020 Aug |
2 |
| 10 |
31653700 | The KDEL receptor has a role in the biogenesis and trafficking of the epithelial sodium channel (ENaC). | 2019 Nov 29 |
2 |
| 11 |
31715083 | Mucus, mucins, and cystic fibrosis. | 2019 Nov |
2 |
| 12 |
31715088 | Anti-inflammatories and mucociliary clearance therapies in the age of CFTR modulators. | 2019 Nov |
1 |
| 13 |
30063865 | Unmet needs in cystic fibrosis. | 2018 Jul |
1 |
| 14 |
30289627 | Rapid therapeutic advances in CFTR modulator science. | 2018 Nov |
1 |
| 15 |
29124052 | Thirty Years of Sweat Chloride Testing at One Referral Center. | 2017 |
1 |
| 16 |
26282188 | CFTR genotype-related body water and electrolyte balance during a marathon. | 2016 Sep |
1 |
| 17 |
27784314 | Quality of sweat test (ST) based on the proportion of sweat sodium (Na) and sweat chloride (Cl) as diagnostic parameter of cystic fibrosis: are we on the right way? | 2016 Oct 26 |
1 |
| 18 |
23897018 | The need for salt: does a relationship exist between cystic fibrosis and exercise-associated hyponatremia? | 2014 Mar |
3 |
| 19 |
24500283 | Reduced GM1 ganglioside in CFTR-deficient human airway cells results in decreased β1-integrin signaling and delayed wound repair. | 2014 May 1 |
2 |
| 20 |
24583165 | CFTR genotype and clinical outcomes of adult patients carried as cystic fibrosis disease. | 2014 May 1 |
2 |
| 21 |
24736260 | [CFTR and ENaC functions in cystic fibrosis]. | 2014 |
1 |
| 22 |
24934256 | A neutrophil intrinsic impairment affecting Rab27a and degranulation in cystic fibrosis is corrected by CFTR potentiator therapy. | 2014 Aug 14 |
1 |
| 23 |
25697321 | [Phenotypic variability of cystic fibrosis: case report of twins with F508/F508 mutation]. | 2014 Jul |
1 |
| 24 |
28510183 | CFTR and TNR-CFTR expression and function in the kidney. | 2014 Jun |
1 |
| 25 |
23749691 | Transepithelial nasal potential difference (NPD) measurements in cystic fibrosis (CF). | 2013 Jan-Mar |
2 |
| 26 |
22442149 | Low temperature and chemical rescue affect molecular proximity of DeltaF508-cystic fibrosis transmembrane conductance regulator (CFTR) and epithelial sodium channel (ENaC). | 2012 May 11 |
1 |
| 27 |
22650116 | Cystic fibrosis. | 2012 Mar-Apr |
1 |
| 28 |
23064458 | Prevalence of ΔF508 mutation in the cystic fibrosis transmembrane conductance regulator gene among cystic fibrosis patients from a Brazilian referral center. | 2012 Nov-Dec |
1 |
| 29 |
21303308 | Cystic fibrosis transmembrane regulator potentiators as promising cystic fibrosis therapies. | 2011 Mar |
2 |
| 30 |
21932505 | Improving outcomes in patients with cystic fibrosis. | 2011 Jul-Aug |
2 |
| 31 |
20522854 | Measurement of nasal potential difference in young children with an equivocal sweat test following newborn screening for cystic fibrosis. | 2010 Jun |
1 |
| 32 |
19017867 | Genetic analysis of Rwandan patients with cystic fibrosis-like symptoms: identification of novel cystic fibrosis transmembrane conductance regulator and epithelial sodium channel gene variants. | 2009 May |
3 |
| 33 |
19131642 | A cystic fibrosis respiratory epithelial cell chronically treated by miglustat acquires a non-cystic fibrosis-like phenotype. | 2009 Aug |
1 |
| 34 |
19329540 | Defective organellar acidification as a cause of cystic fibrosis lung disease: reexamination of a recurring hypothesis. | 2009 Jun |
1 |
| 35 |
18604476 | Cystic fibrosis as a bowel cancer syndrome and the potential role of CK2. | 2008 Sep |
1 |
| 36 |
17572013 | Elevated tear fluid levels of MIP-1alpha in patients with cystic fibrosis. | 2007 Jun |
1 |
| 37 |
17040873 | [Functional characterization of naturally occurring CFTR mutants: interest for cystic fibrosis]. | 2006 Sep-Oct |
2 |
| 38 |
15618459 | The effect of varying tonicity on nasal epithelial ion transport in cystic fibrosis. | 2005 Apr 1 |
1 |
| 39 |
11809721 | Temporal regulation of CFTR expression during ovine lung development: implications for CF gene therapy. | 2002 Jan 15 |
1 |
| 40 |
11809765 | Hyperacidification of cellubrevin endocytic compartments and defective endosomal recycling in cystic fibrosis respiratory epithelial cells. | 2002 Apr 19 |
3 |
| 41 |
11717455 | Molecular basis for defective glycosylation and Pseudomonas pathogenesis in cystic fibrosis lung. | 2001 Nov 20 |
1 |
| 42 |
11715942 | Cationic lipid:pDNA complexes for the treatment of cystic fibrosis. | 1999 Apr |
1 |
| 43 |
9048354 | Cystic fibrosis presenting with hypokalemia and metabolic alkalosis in a previously healthy adolescent. | 1997 Feb |
1 |
| 44 |
9093186 | The cystic fibrosis transmembrane regulator gene is expressed in the human endocervix throughout the menstrual cycle. | 1997 Apr |
1 |
| 45 |
7533790 | Normalization of raised sodium absorption and raised calcium-mediated chloride secretion by adenovirus-mediated expression of cystic fibrosis transmembrane conductance regulator in primary human cystic fibrosis airway epithelial cells. | 1995 Mar |
1 |
| 46 |
7543698 | CFTR as a cAMP-dependent regulator of sodium channels. | 1995 Aug 11 |
2 |