Protein Name glucuronidase beta
Organism Homo sapiens
Gene ID 2990
Gene Symbol


UniProt P08236 (BGLR_HUMAN)
Relationships Total Number of functionally related compound(s) : 859
Total Number of Articles : 981

glucuronidase beta

Gene Summary

This gene encodes a hydrolase that degrades glycosaminoglycans, including heparan sulfate, dermatan sulfate, and chondroitin-4,6-sulfate. The enzyme forms a homotetramer that is localized to the lysosome. Mutations in this gene result in mucopolysaccharidosis type VII. Alternative splicing results in multiple transcript variants. There are many pseudogenes of this locus in the human genome.[provided by RefSeq, May 2014]

  • beta-glucuronidase
  • beta-D-glucuronidase
  • beta-G1
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