Protein Name sulfite oxidase
Organism Homo sapiens
Gene ID 6821
Gene Symbol


UniProt P51687 (SUOX_HUMAN), A0A024RB79 (A0A024RB79_HUMAN)
Relationships Total Number of functionally related compound(s) : 111
Total Number of Articles : 111

sulfite oxidase

Gene Summary

Sulfite oxidase is a homodimeric protein localized to the intermembrane space of mitochondria. Each subunit contains a heme domain and a molybdopterin-binding domain. The enzyme catalyzes the oxidation of sulfite to sulfate, the final reaction in the oxidative degradation of the sulfur amino acids cysteine and methionine. Sulfite oxidase deficiency results in neurological abnormalities which are often fatal at an early age. Alternative splicing results in multiple transcript variants encoding identical proteins. [provided by RefSeq, Jul 2008]

  • sulfite oxidase, mitochondrial
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