Protein Name N-sulfoglucosamine sulfohydrolase (sulfamidase)
Organism Mus musculus
Gene ID 27029
Gene Symbol

Sgsh

UniProt Q9EQ08 (Q9EQ08_MOUSE), Q3URR4 (Q3URR4_MOUSE)
Relationships Total Number of functionally related compound(s) : 13
Total Number of Articles : 20
Description

N-sulfoglucosamine sulfohydrolase (sulfamidase)

Gene Summary

Enables sulfuric ester hydrolase activity. Predicted to be involved in glycosaminoglycan catabolic process and heparan sulfate proteoglycan catabolic process. Predicted to act upstream of or within heparan sulfate proteoglycan metabolic process. Predicted to be located in lysosome. Used to study mucopolysaccharidosis III. Human ortholog(s) of this gene implicated in mucopolysaccharidosis III and mucopolysaccharidosis type IIIA. Orthologous to human SGSH (N-sulfoglucosamine sulfohydrolase). [provided by Alliance of Genome Resources, Apr 2022]

synonyms
  • N-sulphoglucosamine sulphohydrolase
  • sulphamidase
  • 4632406A19Rik
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Properties