CPRiL

SUCLG1

succinate-CoA ligase GDP/ADP-forming subunit alpha

This gene encodes the alpha subunit of the heterodimeric enzyme succinate coenzyme A ligase. This enzyme is targeted to the mitochondria and catalyzes the conversion of succinyl CoA and ADP or GDP to succinate and ATP or GTP. Mutations in this gene are the cause of the metabolic disorder fatal infantile lactic acidosis and mitochondrial DNA depletion. [provided by RefSeq, Feb 2010]

• succinate--CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial
• SCS-alpha
• mitochondrial succinate--CoA ligase [ADP/GDP-forming] subunit alpha
succinate-CoA ligase alpha subunit
succinyl-CoA ligase [ADP/GDP-forming] subunit alpha, mitochondrial
succinyl-CoA ligase [GDP-forming] subunit alpha, mitochondrial
succinyl-CoA synthetase subunit alpha
GALPHA
MTDPS9
SUCLA1