Protein Name bifunctional hydroxyacyl-CoA dehydrogenase/enoyl-CoA hydratase FOX2
Organism Saccharomyces cerevisiae S288C
Gene ID 853878
Gene Symbol

FOX2

UniProt Q02207 (FOX2_YEAST)
Relationships Total Number of functionally related compound(s) : 7
Total Number of Articles : 7
Description

bifunctional hydroxyacyl-CoA dehydrogenase/enoyl-CoA hydratase FOX2

Gene Summary

Enables 3-hydroxyacyl-CoA dehydrogenase (NAD+) activity and enoyl-CoA hydratase activity. Involved in fatty acid beta-oxidation. Located in peroxisome. Used to study lipid metabolism disorder. Human ortholog(s) of this gene implicated in D-bifunctional protein deficiency; Perrault syndrome; and Stiff-Person syndrome. Orthologous to human HSD17B4 (hydroxysteroid 17-beta dehydrogenase 4). [provided by Alliance of Genome Resources, Jul 2025]

synonyms
  • bifunctional hydroxyacyl-CoA dehydrogenase/enoyl-CoA hydratase FOX2
  • YKR009C
  • POX2
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Properties