Protein Name caseinolytic mitochondrial matrix peptidase proteolytic subunit
Organism Mus musculus
Gene ID 53895
Gene Symbol

Clpp

UniProt O88696 (CLPP_MOUSE)
Relationships Total Number of functionally related compound(s) : 21
Total Number of Articles : 9
Description

caseinolytic mitochondrial matrix peptidase proteolytic subunit

Gene Summary

Predicted to enable ATPase binding activity; identical protein binding activity; and peptidase activity. Predicted to be involved in membrane protein proteolysis and protein quality control for misfolded or incompletely synthesized proteins. Located in mitochondrion. Is expressed in several structures, including early conceptus; heart; liver; pancreas; and placenta. Used to study Perrault syndrome. Human ortholog(s) of this gene implicated in Perrault syndrome. Orthologous to human CLPP (caseinolytic mitochondrial matrix peptidase proteolytic subunit). [provided by Alliance of Genome Resources, Jul 2025]

synonyms
  • ATP-dependent Clp protease proteolytic subunit, mitochondrial
  • ClpP caseinolytic peptidase, ATP-dependent, proteolytic subunit
  • caseinolytic peptidase, ATP-dependent, proteolytic subunit homolog
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Properties