Protein Name Dihydrolipoyl dehydrogenase, mitochondrial
Organism Caenorhabditis elegans
Gene ID 178387
Gene Symbol

dld-1

UniProt O17953 (DLDH_CAEEL)
Relationships Total Number of functionally related compound(s) : 3
Total Number of Articles : 1
Description

Dihydrolipoyl dehydrogenase, mitochondrial

Gene Summary

Predicted to enable dihydrolipoyl dehydrogenase (NADH) activity and flavin adenine dinucleotide binding activity. Predicted to be involved in 2-oxoglutarate metabolic process. Predicted to be located in mitochondrial matrix. Predicted to be part of oxoglutarate dehydrogenase complex. Predicted to be active in mitochondrion. Human ortholog(s) of this gene implicated in maple syrup urine disease. Orthologous to human DLD (dihydrolipoamide dehydrogenase). [provided by Alliance of Genome Resources, Jul 2025]

synonyms
  • Dihydrolipoyl dehydrogenase, mitochondrial
  • CELE_LLC1.3
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Properties