galactosylceramidase ; Mus musculus






63 Article(s)
Download
PMID
Title
Journal
Pub. Date
#Total Relationship(s)
1 1280141 Doxorubicin inhibits differentiation and enhances expression of the helix-loop-helix genes Id and mTwi in mouse osteoblastic cells. Biochem Int 1992 Oct 1
2 1706487 Accumulation of galactosylsphingosine (psychosine) does not interfere with phosphorylation and methylation of myelin basic protein in the twitcher mouse. Neurochem Res 1990 Oct 2
3 2066397 Antibody-dependent cellular cytotoxicity in antimyelin antibody-induced oligodendrocyte damage in vitro. J Neuroimmunol 1991 Aug 2
4 2475642 Epidermal growth factor inhibits the expression of myelin basic protein in oligodendrocytes. J Neurosci Res 1989 Aug 1
5 2713667 Lymphokines facilitate maturation of oligodendrocytes in vitro. Brain Res 1989 Feb 20 1
6 3718992 Optimal assay conditions for enzymatic characterization of homozygous and heterozygous twitcher mouse. Biochim Biophys Acta 1986 Jun 11 2
7 6397235 The isolation and long-term culture of oligodendrocytes from newborn mouse brain. Brain Res 1984 Dec 24 2
8 7552298 Schwann cell responses to forskolin and cyclic AMP analogues: comparative study of mouse and rat Schwann cells. Brain Res 1995 May 29 2
9 8101401 Hematopoietic cell transplantation in the twitcher mouse. The effects of pretransplant conditioning with graded doses of busulfan. Transplantation 1993 Jul 2
10 8180787 Progressive dysfunction of twitcher Schwann cells is evaluated better in vitro than in vivo. Brain Res 1994 Feb 21 2
11 8706126 Myelination in the absence of galactocerebroside and sulfatide: normal structure with abnormal function and regional instability. Cell 1996 Jul 26 1
12 8773776 Impairment of protein kinase C activity in twitcher Schwann cells in vitro. Brain Res 1996 Apr 29 2
13 8782879 Age-related differences in mouse Schwann cell response to cyclic AMP. Brain Res 1996 May 6 1
14 8911769 Localization of mRNA for UDP-galactose: ceramide galactosyltransferase in the brain during mouse development. Dev Neurosci 1996 1
15 9384539 Myelin glycolipids and their functions. Curr Opin Neurobiol 1997 Oct 1
16 9514207 Suppressed UDP-galactose: ceramide galactosyltransferase and myelin protein mRNA in twitcher mouse brain. J Neurosci Res 1998 Feb 15 1
17 9530920 New perspectives on the function of myelin galactolipids. Trends Neurosci 1998 Mar 2
18 9560463 Galactosphingolipids and axono-glial interaction in myelin of the central nervous system. Cell Tissue Res 1998 May 1
19 9672425 Galactolipids in the formation and function of the myelin sheath. Microsc Res Tech 1998 Jun 1 2
20 9843152 Demyelination and altered expression of myelin-associated glycoprotein isoforms in the central nervous system of galactolipid-deficient mice. J Neurosci Res 1998 Dec 1 2
21 9878848 Responses to cyclic AMP is impaired in the twitcher Schwann cells in vitro. Brain Res 1999 Jan 23 15
22 10447239 Myelin abnormalities in mice deficient in galactocerebroside and sulfatide. J Neurocytol 1998 Sep 1
23 10739570 Genetic dissection of myelin galactolipid function. J Neurocytol 1999 Apr-May 1
24 10740228 L-cycloserine slows the clinical and pathological course in mice with globoid cell leukodystrophy (twitcher mice). J Neurosci Res 2000 Apr 15 3
25 11883719 Silybin and its bioavailable phospholipid complex (IdB 1016) potentiate in vitro and in vivo the activity of cisplatin. Life Sci 2002 Feb 8 2
26 12111848 Establishment and characterization of spontaneously immortalized Schwann cells from murine model of globoid cell leukodystrophy (twitcher). J Neurosci Res 2002 Jun 1 1
27 12417425 Galactolipids are molecular determinants of myelin development and axo-glial organization. Biochim Biophys Acta 2002 Dec 19 2
28 14730700 Sulfatide is a negative regulator of oligodendrocyte differentiation: development in sulfatide-null mice. Glia 2004 Feb 3
29 15039117 Psychosine-induced apoptosis in a mouse oligodendrocyte progenitor cell line is mediated by caspase activation. Neurosci Lett 2004 Apr 1 1
30 15248301 Analysis of galactocerebrosidase activity in the mouse brain by a new histological staining method. J Neurosci Res 2004 Aug 1 3
31 15707574 Galactosylceramidase deficiency causes sperm abnormalities in the mouse model of globoid cell leukodystrophy. Exp Cell Res 2005 Mar 10 3
32 15813970 Anti-inflammatory therapy by ibudilast, a phosphodiesterase inhibitor, in demyelination of twitcher, a genetic demyelination model. J Neuroinflammation 2005 Apr 6 2
33 15968630 Oligodendrocyte-specific ceramide galactosyltransferase (CGT) expression phenotypically rescues CGT-deficient mice and demonstrates that CGT activity does not limit brain galactosylceramide level. Glia 2005 Nov 15 3
34 16169744 Insulin-like growth factor-1 provides protection against psychosine-induced apoptosis in cultured mouse oligodendrocyte progenitor cells using primarily the PI3K/Akt pathway. Mol Cell Neurosci 2005 Nov 1
35 16759875 Suppression of galactosylceramidase (GALC) expression in the twitcher mouse model of globoid cell leukodystrophy (GLD) is caused by nonsense-mediated mRNA decay (NMD). Neurobiol Dis 2006 Aug 3
36 19397784 Splenic natural killer cell activity in two models of experimental neurodegenerative diseases. J Cell Mol Med 2009 Aug 3
37 19439584 Psychosine accumulates in membrane microdomains in the brain of krabbe patients, disrupting the raft architecture. J Neurosci 2009 May 13 4
38 20441793 Factors that affect postnatal bone growth retardation in the twitcher murine model of Krabbe disease. Biochim Biophys Acta 2010 Jul-Aug 1
39 21871134 Tissue inhibitor of metalloproteinases-3 mediates the death of immature oligodendrocytes via TNF-α/TACE in focal cerebral ischemia in mice. J Neuroinflammation 2011 Aug 29 1
40 22704480 Bone marrow transplantation increases efficacy of central nervous system-directed enzyme replacement therapy in the murine model of globoid cell leukodystrophy. Mol Genet Metab 2012 Sep 1
41 22849820 Oxidative stress as a therapeutic target in globoid cell leukodystrophy. Exp Neurol 2012 Oct 1
42 23404611 MMP-3 mediates psychosine-induced globoid cell formation: implications for leukodystrophy pathology. Glia 2013 May 3
43 23590629 Characterization of adipose-derived stromal/stem cells from the Twitcher mouse model of Krabbe disease. BMC Cell Biol 2013 Apr 16 1
44 23606584 Multipotent stromal cells alleviate inflammation, neuropathology, and symptoms associated with globoid cell leukodystrophy in the twitcher mouse. Stem Cells 2013 Aug 1
45 23611871 Region- and age-dependent alterations of glial-neuronal metabolic interactions correlate with CNS pathology in a mouse model of globoid cell leukodystrophy. J Cereb Blood Flow Metab 2013 Jul 1
46 23755134 Central nervous system pathology progresses independently of KC and CXCR2 in globoid-cell leukodystrophy. PLoS One 2014 2
47 24094551 Characterization and application of a disease-cell model for a neurodegenerative lysosomal disease. Mol Genet Metab 2014 Feb 7
48 24432014 New players in the infertility of a mouse model of lysosomal storage disease: the hypothalamus-pituitary-gonadal axis. Front Endocrinol (Lausanne) 2014 Jan 6 3
49 25236689 Effect of vitamin D3 intake on the onset of disease in a murine model of human Krabbe disease. J Neurosci Res 2015 Jan 8
50 25664578 Morphological and molecular characterisation of Twitcher mouse spermatogenesis: an update. Reprod Fertil Dev 2015 Feb 10 1