Title : Barth syndrome-related cardiomyopathy is associated with a reduction in myocardial glucose oxidation.

Pub. Date : 2021 Jun 1

PMID : 33929899






1 Functional Relationships(s)
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1 Cardiac function and myocardial energy metabolism were assessed via ultrasound echocardiography and isolated working heart perfusions, respectively, in a mouse model of BTHS (doxycycline-inducible Taz knockdown (TazKD) mice). Doxycycline tafazzin, phospholipid-lysophospholipid transacylase Mus musculus