Title : Residual adenylosuccinase activities in fibroblasts of adenylosuccinase-deficient children: parallel deficiency with adenylosuccinate and succinyl-AICAR in profoundly retarded patients and non-parallel deficiency in a mildly retarded girl.

Pub. Date : 1993

PMID : 8412002






1 Functional Relationships(s)
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Compound Name
Protein Name
Organism
1 In type II fibroblasts, ASase is characterized by a similar increase in Km for succinyl-AICAR but by a potent inhibition by KCl and nucleoside triphosphates, and by a normal elution profile. nucleoside triphosphates adenylosuccinate lyase Homo sapiens