Title : Amyotrophic lateral sclerosis and denervation alter sphingolipids and up-regulate glucosylceramide synthase.

Pub. Date : 2015 Dec 20

PMID : 26483191






2 Functional Relationships(s)
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1 Glucosylceramide synthase (GCS), the enzyme responsible for GlcCer biosynthesis, was up-regulated in muscle of SOD1(G86R) mice and ALS patients, and in muscle of wild-type mice after surgically induced denervation. Glucosylceramides UDP-glucose ceramide glucosyltransferase Mus musculus
2 Glucosylceramide synthase (GCS), the enzyme responsible for GlcCer biosynthesis, was up-regulated in muscle of SOD1(G86R) mice and ALS patients, and in muscle of wild-type mice after surgically induced denervation. Glucosylceramides UDP-glucose ceramide glucosyltransferase Mus musculus