Protein Name isovaleryl-CoA dehydrogenase
Organism Rattus norvegicus
Gene ID 24513
Gene Symbol


UniProt P12007 (IVD_RAT)
Relationships Total Number of functionally related compound(s) : 10
Total Number of Articles : 6

isovaleryl-CoA dehydrogenase

Gene Summary

Enables identical protein binding activity and isovaleryl-CoA dehydrogenase activity. Involved in leucine catabolic process. Located in mitochondrial matrix and mitochondrial membrane. Human ortholog(s) of this gene implicated in amino acid metabolic disorder and isovaleric acidemia. Orthologous to human IVD (isovaleryl-CoA dehydrogenase). [provided by Alliance of Genome Resources, Apr 2022]

  • isovaleryl-CoA dehydrogenase, mitochondrial
  • butyryl-CoA dehydrogenase
  • isovaleryl coenzyme A dehydrogenase
Click to show/hide the synonyms