PMID-sentid Pub_year Sent_text comp_official_name comp_offsetprotein_name organism prot_offset 28575497-6 2017 The impact of LRPPRC deficiency was not limited to OXPHOS, but also included impairment of long-chain fatty acid oxidation, a striking dysregulation of the mitochondrial permeability transition pore, and an unsuspected alteration of trans-membrane H2O2 diffusion, which was traced to the ATP synthase assembly defect, and to changes in the lipid composition of mitochondrial membranes. long-chain fatty acid 91-112 leucine rich pentatricopeptide repeat containing Homo sapiens 14-20