Title : Glycogen storage disease type 1a is associated with disturbed vitamin A metabolism and elevated serum retinol levels.

Pub. Date : 2020 Jan 15

PMID : 31813960






1 Functional Relationships(s)
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1 Aberrant expression of genes involved in vitamin A metabolism was associated with reduced basal mRNA levels of markers of inflammation (Cd68, Tnfalpha, Nos2, Il-6) and fibrosis (Col1a1, Acta2, Tgfbeta, Timp1) in livers of L-G6pc-/- mice. vitamin A, vitamin E, vitamin K3 drug combination nitric oxide synthase 2, inducible Mus musculus