Title : Impaired biotinidase activity disrupts holocarboxylase synthetase expression in late onset multiple carboxylase deficiency.

Pub. Date : 2008 Dec 5

PMID : 18845537






4 Functional Relationships(s)
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Compound Name
Protein Name
Organism
1 This latter reaction is catalyzed by holocarboxylase synthetase (HCS) via synthesis of 5"-biotinyl-AMP (B-AMP) from biotin and ATP, followed by transfer of the biotin to a specific lysine residue of the apocarboxylase substrate. Biotin holocarboxylase synthetase Homo sapiens
2 This latter reaction is catalyzed by holocarboxylase synthetase (HCS) via synthesis of 5"-biotinyl-AMP (B-AMP) from biotin and ATP, followed by transfer of the biotin to a specific lysine residue of the apocarboxylase substrate. Biotin holocarboxylase synthetase Homo sapiens
3 This latter reaction is catalyzed by holocarboxylase synthetase (HCS) via synthesis of 5"-biotinyl-AMP (B-AMP) from biotin and ATP, followed by transfer of the biotin to a specific lysine residue of the apocarboxylase substrate. Biotin holocarboxylase synthetase Homo sapiens
4 This latter reaction is catalyzed by holocarboxylase synthetase (HCS) via synthesis of 5"-biotinyl-AMP (B-AMP) from biotin and ATP, followed by transfer of the biotin to a specific lysine residue of the apocarboxylase substrate. Biotin holocarboxylase synthetase Homo sapiens