64 Article(s)Download |
PMID | Title | Pub. Year | #Total Relationships |
51 | 19699305 | A transgenic mouse model of spinocerebellar ataxia type 3 resembling late disease onset and gender-specific instability of CAG repeats. | 2010 Feb | 3 |
52 | 20007218 | Autophagy induction reduces mutant ataxin-3 levels and toxicity in a mouse model of spinocerebellar ataxia type 3. | 2010 Jan | 1 |
53 | 20510362 | Motor uncoordination and neuropathology in a transgenic mouse model of Machado-Joseph disease lacking intranuclear inclusions and ataxin-3 cleavage products. | 2010 Oct | 2 |
54 | 19084066 | In vivo suppression of polyglutamine neurotoxicity by C-terminus of Hsp70-interacting protein (CHIP) supports an aggregation model of pathogenesis. | 2009 Mar | 4 |
55 | 18502140 | Polyglutamine-expanded ataxin-3 causes cerebellar dysfunction of SCA3 transgenic mice by inducing transcriptional dysregulation. | 2008 Jul | 4 |
56 | 18668148 | PolyQ-expanded ataxin-3 interacts with full-length ataxin-3 in a polyQ length-dependent manner. | 2008 Aug | 10 |
57 | 17626202 | Nuclear localization of ataxin-3 is required for the manifestation of symptoms in SCA3: in vivo evidence. | 2007 Jul 11 | 4 |
58 | 17764659 | Inactivation of the mouse Atxn3 (ataxin-3) gene increases protein ubiquitination. | 2007 Oct 26 | 2 |
59 | 16389311 | Mouse models of Machado-Joseph disease and other polyglutamine spinocerebellar ataxias. | 2005 Jul | 2 |
60 | 15537899 | A mutant ataxin-3 putative-cleavage fragment in brains of Machado-Joseph disease patients and transgenic mice is cytotoxic above a critical concentration. | 2004 Nov 10 | 2 |
61 | 11978767 | YAC transgenic mice carrying pathological alleles of the MJD1 locus exhibit a mild and slowly progressive cerebellar deficit. | 2002 May 1 | 1 |
62 | 12127147 | Chemical chaperones reduce aggregate formation and cell death caused by the truncated Machado-Joseph disease gene product with an expanded polyglutamine stretch. | 2002 Jul | 5 |
63 | 11394998 | Genetic ablation of orexin neurons in mice results in narcolepsy, hypophagia, and obesity. | 2001 May | 1 |
64 | 9020849 | Instability of highly expanded CAG repeats in mice transgenic for the Huntington's disease mutation. | 1997 Feb | 2 |