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1 |
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26368820 | Efficient Activation of Pathogenic ΔPhe501 Mutation in Monocarboxylate Transporter 8 by Chemical and Pharmacological Chaperones. | 2015 Dec |
1 |
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1 |
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21525008 | ERp29 regulates DeltaF508 and wild-type cystic fibrosis transmembrane conductance regulator (CFTR) trafficking to the plasma membrane in cystic fibrosis (CF) and non-CF epithelial cells. | 2011 Jun 17 |
1 |
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22069317 | 4-Phenylbutyrate stimulates Hsp70 expression through the Elp2 component of elongator and STAT-3 in cystic fibrosis epithelial cells. | 2011 Dec 30 |
1 |
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18285607 | Chemical rescue of deltaF508-CFTR mimics genetic repair in cystic fibrosis bronchial epithelial cells. | 2008 Jun |
1 |
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18574003 | Proinflammatory effect of sodium 4-phenylbutyrate in deltaF508-cystic fibrosis transmembrane conductance regulator lung epithelial cells: involvement of extracellular signal-regulated protein kinase 1/2 and c-Jun-NH2-terminal kinase signaling. | 2008 Sep |
10 |
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17890229 | Modulation of epithelial sodium channel trafficking and function by sodium 4-phenylbutyrate in human nasal epithelial cells. | 2007 Nov 23 |
2 |
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16472777 | Novel short chain fatty acids restore chloride secretion in cystic fibrosis. | 2006 Mar 31 |
1 |
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16738016 | Phosphorylation of S955 at the protein kinase A consensus promotes maturation of the alpha subunit of the colonic H+,K+ -ATPase. | 2006 Jul |
1 |
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12095312 | Evidence of CFTR function in cystic fibrosis after systemic administration of 4-phenylbutyrate. | 2002 Jul |
1 |
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11164382 | Direct block of the cystic fibrosis transmembrane conductance regulator Cl(-) channel by butyrate and phenylbutyrate. | 2001 Jan 12 |
4 |
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11404244 | Sodium 4-phenylbutyrate downregulates HSC70 expression by facilitating mRNA degradation. | 2001 Jul |
1 |
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11404246 | Induction of HSP70 promotes DeltaF508 CFTR trafficking. | 2001 Jul |
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10666019 | Focus on "Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of DeltaF508-CFTR". | 2000 Feb |
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10666020 | Sodium 4-phenylbutyrate downregulates Hsc70: implications for intracellular trafficking of DeltaF508-CFTR. | 2000 Feb |
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10720936 | Pharmacologic restoration of delta F508 CFTR-mediated chloride current. | 2000 Mar |
1 |
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10853862 | Activation of deltaF508 CFTR in a cystic fibrosis respiratory epithelial cell line by 4-phenylbutyrate, genistein and CPX. | 2000 May |
3 |
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9476862 | A pilot clinical trial of oral sodium 4-phenylbutyrate (Buphenyl) in deltaF508-homozygous cystic fibrosis patients: partial restoration of nasal epithelial CFTR function. | 1998 Feb |
1 |
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3 |