| 1 |
34459410 | Characterization of a Knock-In Mouse Model with a Huntingtin Exon 1 Deletion. | 2021 |
4 |
| 2 |
31282030 | Phenotype onset in Huntington's disease knock-in mice is correlated with the incomplete splicing of the mutant huntingtin gene. | 2019 Dec |
1 |
| 3 |
28211815 | Generation and Characterization of Knock-in Mouse Models Expressing Versions of Huntingtin with Either an N17 or a Combined PolyQ and Proline-Rich Region Deletion. | 2017 |
3 |
| 4 |
22892315 | A series of N-terminal epitope tagged Hdh knock-in alleles expressing normal and mutant huntingtin: their application to understanding the effect of increasing the length of normal Huntingtin's polyglutamine stretch on CAG140 mouse model pathogenesis. | 2012 Aug 14 |
1 |
| 5 |
22956985 | Deletion of the huntingtin proline-rich region does not significantly affect normal huntingtin function in mice. | 2012 |
1 |
| 6 |
19864571 | Intrabody gene therapy ameliorates motor, cognitive, and neuropathological symptoms in multiple mouse models of Huntington's disease. | 2009 Oct 28 |
1 |
| 7 |
17975550 | Mutant huntingtin can paradoxically protect neurons from death. | 2008 Mar |
1 |
| 8 |
17373643 | Mapping of the epitope of monoclonal antibody 2B4 to the proline-rich region of human Huntingtin, a region critical for aggregation and toxicity. | 2007 May |
1 |
| 9 |
16405500 | Interaction of huntingtin fragments with brain membranes--clues to early dysfunction in Huntington's disease. | 2006 Feb |
1 |
| 10 |
15371500 | Activation of the IkappaB kinase complex and nuclear factor-kappaB contributes to mutant huntingtin neurotoxicity. | 2004 Sep 15 |
2 |