polyglutamine

ataxin 3 ; Homo sapiens







175 Article(s)
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151 15504352 Full-length expanded ataxin-3 enhances mitochondrial-mediated cell death and decreases Bcl-2 expression in human neuroblastoma cells. 2004 Nov 26 1
152 15544810 Characterization of the structure and the amyloidogenic properties of the Josephin domain of the polyglutamine-containing protein ataxin-3. 2004 Dec 3 3
153 15639784 Misfolding promotes the ubiquitination of polyglutamine-expanded ataxin-3, the defective gene product in SCA3/MJD. 2004 6
154 12914917 Domain architecture of the polyglutamine protein ataxin-3: a globular domain followed by a flexible tail. 2003 Aug 14 1
155 14661975 Temperature-dependent, irreversible formation of amyloid fibrils by a soluble human ataxin-3 carrying a moderately expanded polyglutamine stretch (Q36). 2003 Dec 16 2
156 15152500 [Mechanisms to control degradation of polyglutamine-containing protein]. 2003 Nov 6
157 12297501 Ataxin-3 is a histone-binding protein with two independent transcriptional corepressor activities. 2002 Nov 22 1
158 12430715 Promyelocytic leukemia protein is redistributed during the formation of intranuclear inclusions independent of polyglutamine expansion: an immunohistochemical study on Marinesco bodies. 2002 Nov 2
159 12460614 Attenuated nuclear shrinkage in neurons with nuclear aggregates--a morphometric study on pontine neurons of Machado-Joseph disease brains. 2002 Nov 1
160 11561037 Preferential recruitment of ataxin-3 independent of expanded polyglutamine: an immunohistochemical study on Marinesco bodies. 2001 Oct 1
161 11563629 Non-expanded polyglutamine proteins in intranuclear inclusions of hereditary ataxias--triple-labeling immunofluorescence study. 2001 Aug 1
162 11572863 The role of protein composition in specifying nuclear inclusion formation in polyglutamine disease. 2001 Nov 30 1
163 11572942 An expanded glutamine repeat destabilizes native ataxin-3 structure and mediates formation of parallel beta -fibrils. 2001 Oct 9 1
164 11719247 Transglutaminase-dependent formation of protein aggregates as possible biochemical mechanism for polyglutamine diseases. 2001 Oct-Nov 1 1
165 11719271 Differential susceptibility of cultured cell lines to aggregate formation and cell death produced by the truncated Machado-Joseph disease gene product with an expanded polyglutamine stretch. 2001 Oct-Nov 1 2
166 10712199 High germinal instability of the (CTG)n at the SCA8 locus of both expanded and normal alleles. 2000 Mar 1
167 10915768 Ataxin-3, the MJD1 gene product, interacts with the two human homologs of yeast DNA repair protein RAD23, HHR23A and HHR23B. 2000 Jul 22 2
168 10928570 The molecular biology of the autosomal-dominant cerebellar ataxias. 2000 Jul 1
169 10993685 Ataxin-3 is translocated into the nucleus for the formation of intranuclear inclusions in normal and Machado-Joseph disease brains. 2000 Oct 1
170 10072437 Evidence for proteasome involvement in polyglutamine disease: localization to nuclear inclusions in SCA3/MJD and suppression of polyglutamine aggregation in vitro. 1999 Apr 4
171 10556285 Ataxin-3 with an altered conformation that exposes the polyglutamine domain is associated with the nuclear matrix. 1999 Dec 7
172 9580663 Ataxin-3 is transported into the nucleus and associates with the nuclear matrix. 1998 Jun 1
173 9852144 Recruitment and the role of nuclear localization in polyglutamine-mediated aggregation. 1998 Dec 14 1
174 10069576 Heterogeneous intracellular localization and expression of ataxin-3. 1998 Nov 2
175 8968739 Screening for proteins with polyglutamine expansions in autosomal dominant cerebellar ataxias. 1996 Dec 1