Title : ADAMTS18 Deficiency Leads to Pulmonary Hypoplasia and Bronchial Microfibril Accumulation.

Pub. Date : 2020 Aug 20

PMID : 32882513






1 Functional Relationships(s)
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1 These developmental defects worsen lipopolysaccharide-induced acute lung injury and bleomycin-induced lung fibrosis in adult Adamts18-deficient mice. Bleomycin a disintegrin-like and metallopeptidase (reprolysin type) with thrombospondin type 1 motif, 18 Mus musculus