Title : Improved metabolic control in tetrahydrobiopterin (BH4), responsive phenylketonuria with sapropterin administered in two divided doses vs. a single daily dose.

Pub. Date : 2017 Jul 26

PMID : 28593914






1 Functional Relationships(s)
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1 BH4 is the co-factor of the enzyme phenylalanine hydroxylase (PAH) and improves PAH activity and, thus, Phe tolerance in the diet. Phenylalanine phenylalanine hydroxylase Homo sapiens