Title : Mitochondrial bioenergetics and dynamics in Huntington's disease: tripartite synapses and selective striatal degeneration.

Pub. Date : 2010 Jun

PMID : 20454921






1 Functional Relationships(s)
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1 Evidence from genetic HD models suggest that mutant huntingtin (mHtt) compromises mitochondrial bioenergetics and dynamics, preventing efficient calcium handling and ATP generation in neuronal networks. Adenosine Triphosphate huntingtin Mus musculus