Title : A cystic fibrosis respiratory epithelial cell chronically treated by miglustat acquires a non-cystic fibrosis-like phenotype.

Pub. Date : 2009 Aug

PMID : 19131642






1 Functional Relationships(s)
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1 Miglustat (N-butyldeoxynojirimycin, Zavesca), an inhibitor of the alpha-1,2 glucosidase, has been proposed for clinical use in CF because of its effect as a corrector of the defective trafficking of F508del-CFTR. miglustat CF transmembrane conductance regulator Homo sapiens